1961年以来日本人曾报导一组脑血管闭塞性疾患,其临床表现与发病的年龄有关,年龄小于20岁的以发作性肢体无力或偏瘫最常见;20岁以上者则以蛛网膜下腔出血多见。脑血管造影的特点是,双侧颈内动脉床突上段狭窄或闭塞,同时在基底节有侧支循环的特殊毛细血管扩张网形成。由于后者的形态仿佛抽烟时喷出的烟雾,故被称为 Moyamoya(即烟雾)病。 Japanese have reported since 1961 a group of cerebrovascular occlusive disease, its clinical manifestations and the age of onset, age less than 20 years of onset of limb weakness or hemiplegia is the most common; 20-year-old who were subarachnoid hemorrhage More common. Cerebrovascular angiography is characterized by narrowing or occlusion of the superior segment of the bilateral internal carotid artery and formation of a special capillary dilatation network with collateral circulation in the basal ganglia. The latter is called Moyamoya (smog) because it looks like the smoke it emits when it is smoked.