产后溶血性尿毒症综合征是指在产后以急性微血管病性溶血性贫血、血小板减少及急性肾功能衰竭三大特征为主的危重性综合征。病因与妊娠期凝血功能异常、机械性因素、遗传、免疫及感染等因素有关。其发病机制是肾脏局部的微血管病性溶血及血管内凝血。该综合征虽然发生率极低,但由于发病急,进展快,病死率高,应引起临床高度重视,不断提高对本病的认识,力求做到早诊断、早治疗、争取改善预后。 Postpartum hemolytic uremic syndrome refers to postpartum with acute microangiopathic hemolytic anemia, thrombocytopenia and acute renal failure of the three major features of the critical syndrome. Etiology and coagulation disorders during pregnancy, mechanical factors, genetic, immune and infection and other factors. The pathogenesis of renal microvascular hemolysis and intravascular coagulation. Although the incidence of this syndrome is extremely low, due to its acute onset, rapid progression and high mortality rate, it should arouse great attention in the clinic and continuously raise awareness of this disease so as to achieve early diagnosis and early treatment and strive to improve the prognosis.