先天性无阴道是女性生殖器官发育畸形的一种。是胚胎在发育时期受到内在或外界因素阻扰导致副中肾导管发育异常所致。以阴道缺如、子宫未发育(仅有双角残留物),而输卵管、卵巢女性第二性征以及全身生长均正常为特征,其发生率为1:5000。由于此病的特殊性,使患者心态非常复杂。临床应根据病人的心身特点实施护理,才能保障心身健康。 Congenital absence of vagina is a genital malformation of the female. Is the embryo in the developmental period by internal or external factors obstruction caused by the deputy of renal duct dysplasia caused. Vaginal absence, the uterus is not developed (only two-residue residues), while the fallopian tube, ovarian secondary sexual characteristics and systemic growth were normal, characterized by the incidence of 1: 5000. Due to the particularity of the disease, the patient’s psychology is very complicated. Clinical care should be based on the characteristics of the patient’s body and mind, in order to protect mental and physical health.