骨外黏液样软骨肉瘤(extraskeletal myxoid chondrosarcoma,EMC)是一种罕见的恶性软组织肿瘤,在所有软组织肉瘤中比例不足3%,由于不能说明该肿瘤有软骨分化,所以WHO(2002)肿瘤分类中,将其归为分化未定的肿瘤[1],目前国内仅有少数个案报道。近期我院收治EMC患者1例,报道如下。1临床资料患者,男,47岁,主因4年前无明显诱因发现右小腿肿物 Extraskeletal myxoid chondrosarcoma (EMC) is a rare malignant soft tissue tumor with less than 3% of all soft tissue sarcomas. Since there is no evidence of cartilage differentiation, the WHO (2002) classification of tumors, Will be classified as undetermined tumor differentiation [1], at present there are only a few cases reported. Recently, our hospital admitted to EMC patients in 1 case, reported as follows. 1 clinical data of patients, male, 47 years old, mainly due to no obvious incentive 4 years ago found the right calf mass