先天性阴道缺如的发生率为1/4 000~1/5 000,其中仅7%~8%为阴道闭锁,伴正常发育子宫体。在阴道发育异常患者中,先天性子宫阴道缺如患者已有很多手术治疗方式,国内外文献报道的常用方法有乙状结肠代阴道、腹膜代阴道、各种生物材料代阴道等。而先天性阴道闭锁合并有正常子宫患者少见,可借鉴的手术经验很少,手术方式也不统一,争议颇多。发病年龄早,刚进入青春期不久就出现规律性腹痛、盆腔包块等临床症状,外阴发育尚不成熟等是治疗的难点。理想的治疗方案不仅要解决其月经血通畅流出的生理功能,还要在首次手术的同时就能兼顾完成其将来的生殖功能。目前文献报道的方法有子宫切 Congenital vaginal absence of the incidence of 1/4 000 to 1/5 000, of which only 7% to 8% of vaginal atresia, with the normal development of the uterus. In patients with vaginal dysplasia, congenital uterine absence of patients with a lot of surgical treatment has been the literature reports at home and abroad commonly used methods of sigmoid colon on behalf of the vagina, peritoneal vagina, a variety of biological materials on behalf of the vagina. The congenital vaginal atresia combined with normal uterine patients rare, little experience in surgery can be learned, the surgical approach is not uniform, a lot of controversy. Early onset of adolescence, just entered the adolescent period of regular abdominal pain, pelvic mass and other clinical symptoms, vulvar development is not yet mature is the treatment of difficult. The ideal treatment is not only to solve the menstrual flow of menstrual flow out of the physiological function, but also in the first surgery can take into account the completion of its future reproductive function. The method reported in the literature is hysterectomy