目的　探讨小儿先天性心瓣膜病手术治疗的方法 ,并总结其经验。　方法　 45例先天性心瓣膜病患儿实施主动脉瓣修复成形术 4例 ,二尖瓣综合成形术 31例 ,二尖瓣置换术、三尖瓣置换术和主动脉瓣环扩大瓣膜置换术各1例 ,三尖瓣综合成形术 9例次。外科技术包括瓣叶或交界折叠 (悬吊 )成形 ,瓣环环缩 ,置 Carpentier环 ,升主动脉加宽换瓣 ,瓣叶楔形切除及瓣下结构畸形修复等 ,同期矫治其它心内畸形。　结果　 1例术后死于重度低心排血量综合征 ,其余 44例顺利恢复。二维超声心动图示 5例有轻度二尖瓣反流 ,1例有轻度三尖瓣反流 ,随访 5个月～ 8年 ,效果稳定。　结论　采用综合成形技术 ,保留自身瓣膜是小儿先天性心瓣膜病外科治疗的首选方法 ,具有效果确切 ,术后心功能好 ,并发症少 ,无需长期抗凝及不影响生长发育等优点。 Objective To investigate the surgical treatment of children with congenital heart valve disease and to summarize its experience. Methods 45 cases of congenital heart valve disease in children underwent aortic valve repair angioplasty in 4 cases, mitral valve plasty in 31 cases, mitral valve replacement, tricuspid valve replacement and aortic annulus valve replacement 1 case, tricuspid valve plasty in 9 cases. Surgical techniques include valve leaflets or junction fold (suspension) forming, ring annulus contraction, setting Carpentier ring, widening aortic valve replacement, valve leaflet wedge resection and deformity repair under the valve, the same period correction of other cardiac malformations. Results 1 patient died of severe low cardiac output syndrome, the remaining 44 patients recovered successfully. Two-dimensional echocardiography showed mild mitral regurgitation in 5 cases and mild tricuspid regurgitation in 1 case. The follow-up was from 5 months to 8 years with stable results. Conclusion The use of integrated forming technology to retain their own valve is the preferred method of surgical treatment of children with congenital heart valve disease, with the exact effect, good cardiac function, fewer complications, no long-term anticoagulation and does not affect the growth and development advantages.