肝脏恶性问质肿瘤是十分罕见的。作者报告31例肝脏原发性未分化型肉瘤。这类肉瘤主要发生于儿童年龄组,其中27例(87.1%)发生于15岁以下,无性别,种族地区差异。其中28例主诉为腹部包块和/或腹痛,其余3例为发烧。初次物理检查在上腹部和/或右上象限均可触及肿块。患者均行剖腹探查,初次术中发现2例肿瘤破裂,其余肿瘤肝外播散。其中20例进行肿瘤大小测 Malignant liver tumor is very rare. The authors report 31 cases of primary undifferentiated liver sarcoma. The majority of these sarcomas occurred in the children’s age group, with 27 (87.1%) occurring under the age of 15 years without genders and racial differences. Of the 28 cases, the main complaint was abdominal mass and / or abdominal pain, and the remaining 3 patients had fever. Initial physical examination in the upper abdomen and / or upper right quadrant palpable mass. Patients underwent exploratory laparotomy, the first intraoperative findings of 2 cases of tumor rupture, the rest of the tumor spread outside the liver. Twenty of these patients underwent tumor size measurement