目的 :研究促结缔组织增生性成釉细胞瘤的临床病理特点。方法 :对 13例促结缔组织增生性成釉细胞瘤进行临床病理研究及病例随访。结果 :13例中女多于男 (1.2∶1) ,平均年龄 45岁 ,上下颌之比为 1∶1.2。病变主要位于前牙区和 /或前磨牙 (77% )。X线表现通常为透射影、阻射影混存。镜下以大量增生的纤维结缔组织间质中散在不规则、压缩状上皮岛或条索为特点。结论 :促结缔组织增生性成釉细胞瘤为成釉细胞瘤的一种新的类型 ,具有特征性病理表现及低复发率。 Objective: To study the clinicopathological features of connective tissue proliferative ameloblastoma. Methods : Thirteen cases of connective tissue proliferative ameloblastoma were studied by clinical pathology and follow-up. Results: Among the 13 cases, women were more than men (1.2:1), the average age was 45 years, and the ratio between upper and lower jaws was 1:1.2. The lesions were mainly located in the anterior region and/or premolars (77%). X-ray manifestations are usually transmission shadows and shadow shadows. Under the microscope, a large number of hyperplastic fibrous connective tissue interspersed in irregular, compressed epithelial islands or strips are characteristic. Conclusion : The connective tissue proliferative ameloblastoma is a new type of ameloblastoma with characteristic pathological features and low recurrence rate.