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根据组织学的特征,目前将间质性肺炎分成下列5种类型:(1)通常的间质性肺炎(Usually interstitial pneumonia,UIP);(2)脱屑性间质性肺炎(Desquamatire interstitial pneumonia,DIP);(3)伴有弥漫性肺泡损伤的阻塞性细支气管炎(Bronchiolitis obliterans with diffuse alveolar damage);(4)淋巴样间质性肺炎(Lymphoid interstitial pneumonia);(5)巨细胞间质性肺炎(Giantcell interstitial pneumonia)。其中以UIP最常见,DIP次之。DIP的名称和概念是Liebow等于1965年首先提出的,由于其病理改变、X线特征、对治疗的反应性及预后等方面均有别于其他类型的间质性肺炎,因而成为一种独立的疾病。
According to histological features, interstitial pneumonia is currently divided into the following five types: (1) the usual interstitial pneumonia (Usually interstitial pneumonia, UIP); (2) desquamative interstitial pneumonia (Desquamatire interstitial pneumonia, DIP); (3) Bronchiolitis obliterans with diffuse alveolar damage; (4) Lymphoid interstitial pneumonia; (5) giant cell mesenchymal Pneumonia (Giantcell interstitial pneumonia). UIP is most common among them, followed by DIP. The name and concept of DIP is first proposed by Liebow et al. In 1965, and is distinguished from other types of interstitial pneumonia by its pathological changes, radiographic features, responsiveness to treatment, and prognosis disease.