主动脉弓中断(interrupted aortic arch,IAA)常合并有动脉导管未闭室间隔缺损、主肺动脉窗等[1]。国外报道在活产新生儿中的发病率占先天性心脏病的1%[2-3]。患儿多伴有严重的心力衰竭或肺动脉高压,病死率高,需尽早手术治疗[4-5]。笔者所在科室于2006-10/2013-06月对30例主动脉弓中断合并心内外畸形婴幼儿行一期矫治术,现就其术中麻醉体会报告 Aortic arch interrupted (interrupted aortic arch, IAA) often associated with patent ductus arteriosus ventricular septal defect, the main pulmonary artery window [1]. Foreign reports in live births in the incidence of congenital heart disease accounted for 1% [2-3]. Children with severe heart failure or pulmonary hypertension, high mortality, surgical treatment as soon as possible [4-5]. The author’s department in 2006-10 / 2013-06 on 30 cases of aortic arch interrupted intra-heart and anomalies infants and young children underwent an orthodontic treatment, now on its intraoperative anesthesia will report