Q—T 间期延长综合征(以下简称 LQTS)并非罕见的疾患,国内文献迄今已报道15例,国外文献到1980年为止已报道539例。可以肯定未报道的病例以及误诊的病例远远超过已报道的病例数。此病如未得到适宜的治疗,病死率为78%,为儿童、青年猝死的重要原因之一;如能得到正确的治疗,则病死率可降至6%左右,故临床医生对此病确有提高认识的必要。 Q-T prolongation syndrome (LQTS) is not a rare disease. Up to date, 15 cases have been reported in domestic literature and 539 cases reported by foreign literature up to 1980. It is certain that unreported cases and misdiagnosed cases far exceed the reported number of cases. If the disease has not been properly treated, the case fatality rate was 78% for children, one of the major causes of sudden death in young people; if the right treatment can be, the case fatality rate can be reduced to about 6%, so clinicians correct There is a need to raise awareness.