1980年世界卫生组织专题小组会议将原发性心肌病分为三大类型:(1)肥厚型;(2)梗阻型;(3)限制型。家族性心肌病绝大多数属肥厚型,很少有充血型者。肥厚型心肌病的特征是:室间隔显著的可伴有不对称性的增厚,室间隔心肌结构的广泛紊乱,轻度至中度的左室游离壁增厚,常伴有左室有时右室流出道梗阻。 The 1980 World Health Organization panel divided primary cardiomyopathy into three major types: (1) hypertrophic; (2) obstructive; (3) restricted. The vast majority of familial cardiomyopathy is hypertrophic, very few congestive people. Hypertrophic cardiomyopathy is characterized by significant ventricular septal thickening that may be accompanied by asymmetry, extensive disorganization of the interventricular septal myocardium, mild to moderate left ventricular free wall thickening, often accompanied by left ventricular sometimes right Outflow tract obstruction.