多发性肌炎(polymyositis,PM)是一种系统性横纹肌炎性肌病,常合并肺间质病变(interstitial lung disease,ILD),严重影响患者预后,呼吸系统受累是PM患者住院及死亡的主要原因。肺间质病变可以是PM的首发症状,作者医院收治1例以肺间质病变为首发症状的PM患者,现将诊疗经验报道如下。1病例资料患者,男,51岁,因“咳嗽、气短2月余,间断胸痛1月余”入院。患者2个多月前无明显诱因出现咳嗽、气 Polymyositis (PM) is a systemic myotubular myopathic myopathy, often associated with interstitial lung disease (ILD), seriously affecting the prognosis of patients, respiratory system involvement is the mainstay of hospitalization and death of PM patients the reason. Pulmonary interstitial disease can be the first symptom of PM, the author admitted to the hospital in 1 cases of interstitial lung disease as the first symptom of PM patients, now the experience of diagnosis and treatment are reported as follows. 1 case data patients, male, 51 years old, because of “cough, shortness of breath more than 2 months, intermittent chest pain more than 1 month ” admitted. No obvious incentive for patients more than 2 months cough, gas