小肠淋巴管扩张症(intestinal lymphangiectasia,IL)是一种罕见病,由Waldmanin[1]于1961年首次报道。该病以小肠淋巴管回流受阻,肠淋巴管和/或乳糜管扩张、破裂,淋巴液漏出为特征,最终导致该病特征性的临床表现,即低蛋白血症、低γ-球蛋白血症、非对称性水肿、浆膜腔积液和淋巴 Intestinal lymphangiectasia (intestinal lymphangiectasia, IL) is a rare disease, first reported by Waldmanin [1] in 1961. The disease is characterized by obstruction of lymphatic drainage of the small intestine, dilatation and rupture of the intestinal lymphatic and / or chylomicrons, and leakage of lymphatic fluid, which eventually leads to the characteristic clinical manifestations of the disease, hypoproteinemia, hypo-gammaglobulinemia , Asymmetric edema, serosal effusion and lymph