我们遇见1例骨-肌型肝豆状核变性,自发病至确诊历时8年,特报道如下。 张×,男,23岁,缓慢进行性双下肢无力12年余,说话迟缓伴流涎4年,于1978年3月24日入院。1965年9月起,患者自觉走路不快并伴足跟部疼痛。此后2年内疼痛延及双膝及髋部,但始终不伴关节红肿。检查抗“O”、血沉 We met one case of bone - myogenic hepatolenticular degeneration, since the onset to the diagnosis lasted 8 years, especially reported as follows. Zhang ×, male, 23 years old, slow progressive weakness in both lower extremities more than 12 years, slow speech with salivation for 4 years, on March 24, 1978 admission. Since September 1965, patients consciously walk unpleasantly and accompanied by heel and foot pain. Pain was delayed for knees and hips in the next two years, but the joint was not swollen all the time. Check against “O”, ESR