隐原性纤维化性肺泡炎的死亡率很高,半数患者确诊后的存活期不超过5年。治疗旨在抑制其炎症过程和限制肺泡的损害和纤维化的发展,常用药物为皮质类固醇,用药后主客观症状改善的百分率分别约为50%和15%.对皮质类固醇治疗无效的患者,使用免疫抑制剂(如硫唑嘌呤、环磷酰胺和苯丁酸氮芥)亦有一定疗效.对10例病因不明的间质性肺疾病患者,使用小剂量环孢菌素 A 治疗的结果进行了回顾性研究。所有患者的诊断均由肺组织活检证实,其中9例在就诊时和随访期间作了支气管肺泡灌洗液的检查。根据最初的 The mortality rate of cryptogenic fibrosis alveolitis is very high, half of the patients after diagnosis of survival of not more than 5 years. Treatment aimed to inhibit its inflammatory processes and to limit the development of alveolar damage and fibrosis, commonly used drugs for corticosteroids, subjective and objective symptoms after treatment were improved by about 50% and 15%, respectively, for corticosteroid therapy ineffective patients, the use of Immunosuppressive agents (such as azathioprine, cyclophosphamide and chlorambucil) also had some efficacy, and in 10 patients with interstitial lung disease of unknown etiology, the results of low-dose cyclosporin A treatment Retrospective study. All patients were diagnosed by biopsy of lung tissue, of which 9 were examined for bronchoalveolar lavage fluid during the visit and during follow-up. According to the original