脊索瘤 (chordoma)为先天性肿瘤 ,来源于胚胎脊索残余。原发于小脑内非常罕见 ,我院发现 1例 ,经手术证实 ,报告如下。男 ,2 3岁 ,间断头痛、头晕 2个月 ,无视物旋转及吞咽呛咳。体检 :双侧视乳头水肿 ,无肢体活动障碍及共济失调。CT表现 :右侧小脑半球及蚓部可见一椭圆形低密 Chordoma is a congenital tumor derived from the spinal cord residual. Primary in the cerebellum is very rare, found in our hospital in 1 case, confirmed by surgery, the report is as follows. Male, 23 years old, intermittent headache, dizziness 2 months, ignoring the rotation and swallowing cough. Physical examination: bilateral papilla edema, no physical activity disorders and ataxia. CT performance: the right cerebellar hemispheres and vermis showed an oval low density