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维思多复为我国第二代氨基酸混合法苯丙酮尿症治疗专用奶粉。本文对21例苯丙酮尿症患儿长期随访结果显示:疗效满意,患儿发育良好,目前DQ或IQ为93.6±15.2,较来院时明显提高(P<0.001)。其中4例新生儿筛查发现的患儿疗效最佳,目前,DQ平均为117.7±5.9。成分分析结果:蛋白质、脂肪、碳水化合物含量分别为16.1±0.8,15.0±0.5,60.4±3.1g/100g,苯丙氨酸为0,18种氨基酸比例合理,含量稳定,既可保证充足的蛋白质等营养供给,也为患儿提供了更多的余地添加辅食。
Weisiduo complex for the second generation of amino acid mixed phenylketonuria treatment for milk powder. Long-term follow-up of 21 patients with phenylketonuria showed satisfactory efficacy and well-developed children. The current DQ or IQ was 93.6 ± 15.2, which was significantly higher than that of the time of admission to hospital (P <0.001). Four of these neonates were found to be most effective in screening children, and the mean DQ was 117.7 ± 5.9 at present. Composition analysis results showed that the content of protein, fat and carbohydrate were 16.1 ± 0.8,15.0 ± 0.5 and 60.4 ± 3.1g / 100g, respectively. The phenylalanine had 0,18 kinds of amino acids with reasonable proportion and stable content, which could ensure sufficient protein Such as nutritional supply, but also for children with more room to add food supplement.