作者报告一组在临床上与肌萎缩侧索硬化症、进行性脊髓性肌萎缩等肌肉萎缩性疾患不同的疾病,命名为青年人非进行性手及前臂限局性肌萎缩症。发病年龄为14～24岁的青年,此为本病重要特征之一。男性居多(37/38)。一侧上肢萎缩者占绝大多数(33/38),双侧上肢对称性肌萎缩者3例,一侧萎缩重于另一侧者2例。虽然以一侧上肢肌萎缩为特征,但在双侧相应部位所作肌电图检查大多数表现出神经元 The authors report a group of diseases that are clinically distinct from muscular atrophic disorders such as amyotrophic lateral sclerosis and progressive spinal muscular atrophy and are named as non-procedural and forearm ABM in young adults. The age of onset of 14 to 24-year-old youth, this is one of the important features of this disease. Most men (37/38). One side of the upper limb atrophy accounted for the vast majority (33/38), bilateral upper limb symmetry muscle atrophy in 3 cases, one side of the atrophy heavier on the other side in 2 cases. Although characterized by one-sided upper extremity muscle atrophy, the majority of EMG examinations performed at the corresponding sites on both sides showed neuronal