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神经性肌萎缩合并视神经萎缩和神经性耳聋尚未见有报道。今将我们所遇到一例,报告如下: 患者刘××,男性,26岁,农民。1977年8月无诱因出现双眼发花,视力逐渐下降至0.7,9月双耳听力减退,某医院按神经性耳聋治疗不见好转。79年1月双手肌肉萎缩,干活无力。家族中无类似疾病发生。81年7月16日来我科门诊检查:神清,语言流利,眼球各方向运动充分,无面瘫,双手骨间肌、大小鱼际肌轻度萎缩,无共济失调及深浅感觉障碍。双弓形足。肱二、三头肌反射消失。脖、踝反射明显减弱,未引出病理反射。眼科会诊:双眼视神经萎缩。7月20日肌电图检查示神经原性损害。脑脊液检查正常。初诊神经性帆萎缩。服用维生素B族药物冶疗。
Neuromuscular atrophy with optic atrophy and neurological deafness have not been reported. Now we will encounter an example, the report is as follows: Patients Liu × ×, male, 26 years old, farmer. There was no incentive in August 1977, eyes blossoming, visual acuity decreased to 0. 7, hearing loss in both ears in a hospital by neurological deafness treatment did not improve. January 79 hands muscle contraction, poor work. No similar disease in the family. July 16, 81 to our clinic for examination: God clear, fluent language, eye movement in all directions, no facial paralysis, hands interosseous muscle, the size of the atresia muscle mild atrophy, no ataxia and depth sensory disturbances. Double bow-shaped foot. Brachial, triceps reflex disappeared. Neck, ankle reflex significantly reduced, did not lead to pathological reflex. Eye consultation: binocular optic atrophy. July 20 Electromyography showed neurogenic damage. Cerebrospinal fluid examination was normal. Newly diagnosed nervous sail atrophy. Take vitamin B family medicine treatment.